{"id":71483,"date":"2017-11-07T15:28:19","date_gmt":"2017-11-07T15:28:19","guid":{"rendered":"http:\/\/humanitasnet-new.local\/malattie\/hemohromatoza\/"},"modified":"2025-01-13T02:58:50","modified_gmt":"2025-01-13T02:58:50","slug":"hemohromatoza","status":"publish","type":"disease","link":"https:\/\/humanitas-net.humweb.webiz.team\/sr\/diseases\/hemohromatoza\/","title":{"rendered":"Hemohromatoza"},"content":{"rendered":"<p>Hemohromatoza je nasledni poreme\u0107aj koji prouzrokuje da telo apsorbuje vi\u0161ak gvo\u017e\u0111a iz hrane. Vi\u0161ak gvo\u017e\u0111a se obi\u010dno skladi\u0161ti u jetri, srcu i pankreasu. Ovo mo\u017ee biti otrovno za organe i da pove\u0107a rizik za dobijanje stanja koja su opasna po \u017eivot, kao \u0161to su rak, ciroza ili sr\u010dane aritmije.<\/p>\n<p>Hemohromatoza je naj\u010de\u0161\u0107a genetska bolest kod belaca; me\u0111utim, mali broj slu\u010dajeva se razvije u opasne komplikacije.<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"simptomi\">Simptomi<\/h2>\n<p>Obi\u010dni simptomi hemohromatoze uklju\u010duju:<\/p>\n<p>Bol u zglobovima<\/p>\n<p>Umor<\/p>\n<p>Slabost<\/p>\n<p>&nbsp;<\/p>\n<p>Po\u010detni simptomi ove bolesti kod mu\u0161karaca moju da se pojave kao rezultat o\u0161te\u0107enja organa i uklju\u010duju:<\/p>\n<p>Bol u zglobovima<\/p>\n<p>Dijabetes<\/p>\n<p>Smanjena potreba za seksom<\/p>\n<p>Impotenciju<\/p>\n<p>Prestanak rada srca<\/p>\n<p>Nalsedna hemahromatoza je prisutna na ro\u0111enju ali simptomi se obi\u010dno pojavljuju kasnije tokom \u017eivota. Kod \u017eena je ve\u0107a verovatno\u0107a da se pojave simptomi nakon menopause jer one vi\u0161e ne gube gvo\u017e\u0111e prilikom menstruacija ili trudno\u0107a.<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"uzroci\">Uzroci<\/h2>\n<p>Nalsedna hemahromatoza je prouzrokovana mutacijom gena koji reguli\u0161e gvo\u017e\u0111e koje apsorbuje telo. Genetska mutacija se prenosi sa roditelja na decu. Genetska mutacija nalsedne hemahromatoze uklju\u010duje HFE gen, koji ima 2 \u010deste mutacije, C282Y i H63D. Jedna od genetskih mutacija se nalazi u ve\u0107ini slu\u010dajeva nalsedne hemahromatoze. Nalsedna hemahromatoza zahteva 2 abnormalna gena, koji se nasle\u0111uju od oba roditelja dok jedan abnormalni gen \u010dini jednu osobu nosiocem genetske mutacije.<\/p>\n<p>&nbsp;<\/p>\n<p>Drugi tipovi hemohromatoze<\/p>\n<p>De\u010dija hemohromatoza: Ovaj poreme\u0107aj je prouzrokovan mutacijom HJV gena i prouzrokuje iste simptome nasledne hemohromatoze kod mladih ljudi starosti izme\u0111u 15 i 30.<\/p>\n<p>Neonatalna hemohromatoza: Neonatalna hemohromatoza se smatra te\u0161kim autoimunim poreme\u0107ajem koji prouzrokuje brzu akumulaciju gvo\u017e\u0111a u jetri i razvojnom fetusu.<\/p>\n<p>Sekondarna hemohromatoza: Sekondarna hemohromatoza se ne nasle\u0111uje ve\u0107 je sama akumulacija gvo\u017e\u0111a rezultat druge bolesti kao \u0161to je hroni\u010dna bolest jetre, infekcije ili anemija.<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"faktori-rizika\">Faktori rizika<\/h2>\n<p>Faktori rizika nalsedne hemahromatoze uklju\u010duju:<\/p>\n<p>2 primerka mutiranog HFE gena<\/p>\n<p>Porodi\u010dna istorija bolesti<\/p>\n<p>Nacionalnost (ljudi poreklom iz Severne Evrope)<\/p>\n<p>Pol (ve\u0107a je verovatno\u0107a da mu\u0161karci razviju simptome za ovu bolest)<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"komplikacije\">Komplikacije<\/h2>\n<p>Nalsedna hemahromatoza mo\u017ee da prouzrokuje brojne simptome ukoliko se ne le\u010di, uklju\u010duju\u0107i:<\/p>\n<p>Problemi sa jetrom: Trajno o\u0161te\u0107enje jetre ili ciroza mogu da se pojave kao rezultat ovog poreme\u0107aja a mogu tako\u0111e da dovedu do raka jetre ili drugih komplikacija.<\/p>\n<p>Problemi sa pankreasom: O\u0161te\u0107enja pankreasa mogu da dovedu do dijabetesa.<\/p>\n<p>Problemi sa srcem: Previ\u0161e gvo\u017e\u0111a u srcu prouzrokuje pote\u0161ko\u0107e srcu prilikom cirkulacije dovoljno krvi. Ovo se zove kongestivni prestanak rad srca. Hemohromatoza mo\u017ee tako\u0111e da prouzrokuje sr\u010dane aritmije, koje mogu da dovedu do podrhtavanja srca, bolova u grudima i nesvestice.<\/p>\n<p>Reprodruktivni problemi: Vi\u0161ak gvo\u017e\u0111a mo\u017ee da prouzrokuje problem sa erekcijom i gubitak \u017eelje za seksom kod mu\u0161karaca i gubljenje menstrualnih ciklusa kod \u017eena.<\/p>\n<p>Promene boje na ko\u017ei: Gvo\u017e\u0111e se skladi\u0161ti u \u0107elijama ko\u017ee i mo\u017ee da u\u010dini da se ko\u017ea \u010dini bronzanom ili sivom.<\/p>\n","protected":false},"featured_media":0,"template":"","class_list":["post-71483","disease","type-disease","status-publish","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v24.3 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Hemohromatoza - Humanitas.net<\/title>\n<meta name=\"robots\" content=\"noindex, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<meta property=\"og:locale\" content=\"sr_RS\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Hemohromatoza - Humanitas.net\" \/>\n<meta property=\"og:description\" content=\"Hemohromatoza je nasledni poreme\u0107aj koji prouzrokuje da telo apsorbuje vi\u0161ak gvo\u017e\u0111a iz hrane. 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