{"id":71458,"date":"2017-11-08T13:34:42","date_gmt":"2017-11-08T13:34:42","guid":{"rendered":"http:\/\/humanitasnet-new.local\/malattie\/maligni-tumori-omotacha-perifernih-nerava\/"},"modified":"2025-01-13T02:58:28","modified_gmt":"2025-01-13T02:58:28","slug":"maligni-tumori-omotacha-perifernih-nerava","status":"publish","type":"disease","link":"https:\/\/humanitas-net.humweb.webiz.team\/sr\/diseases\/maligni-tumori-omotacha-perifernih-nerava\/","title":{"rendered":"Maligni tumori omota\u010da perifernih nerava"},"content":{"rendered":"<h2 id=\"definicija\">Definicija<\/h2>\n<p>Maligni tumori omota\u010da perifernih nerava, ili neurofibrosarkomi, predstavljaju vrstu sarkoma koji poti\u010du iz protektivne vrste nerava koji se \u0161ire iz ki\u010dmene mo\u017edine u druge delove tela. Mogu se pojaviti bilo gde u organizmu, ali naj\u010de\u0161\u0107i slu\u010dajevi poti\u010du iz dubljih struktura gornjih i donjih ekstremiteta kao i trupa. Izazivaju bol i slabost, ponekad i pojavu nodusa. Ovi tumori naj\u010de\u0161\u0107i su me\u0111u osobama sa hereditarnim predispozicijama za razvoj tumora nerava kao i kod osoba podvrgnutih radijacionoj terapiji usled prisustva karcinoma. Ova vrsta tumora tretira se hirur\u0161kim pristupom, te hemoterapijom i radijacionom terapijom u odre\u0111enim slu\u010dajevima.<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"simptomi\">Simptomi<\/h2>\n<p>Simptomi podrazumevaju:<\/p>\n<p>Neurolo\u0161ke simptome<\/p>\n<p>Osetljivost regije u kojoj je tumor lokalizovan<\/p>\n<p>Otok donjih ekstremiteta (naj\u010de\u0161\u0107e bezbolan)<\/p>\n<p>Probleme koji zahvataju afecirane ekstremitete<\/p>\n<p>Bol<\/p>\n<p>Diskomfor<\/p>\n<p>Utrnulost<\/p>\n<p>Pe\u010denje<\/p>\n<p>Vrtoglavicu<\/p>\n<p>Gubitak ravnote\u017ee<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"uzroci\">Uzroci<\/h2>\n<p>Veruje se da neurofibrosarkom nastaje usled genetske predispozicije\u00a0 u porodici.\u00a0 p 53 je tumor supresorni gen koji je lociran na kratkom kraku hromozoma 17 kod pacijenata sa neurofibrosarkomom, te usled njjegove mutacije postoji pove\u0107ana verovatno\u0107a za nastanak tumora. Osobe sa inaktivisanim p53 genom ne poseduju normalan p53 gen koji reguli\u0161e \u0107elijski rast i inhibira nekontrolisan \u0107elijski rast u zdravoj populaciji,\u00a0 te su podlo\u017eniji nastanku tumora. Ipak, ta\u010dan etiopatogenetski mehanizam jo\u0161 uvek nije utvr\u0111en.<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"lecenje\">Le\u010denje<\/h2>\n<p>Terapeutski pristup le\u010denju malignih tumora perifernih nerava jeste hirur\u0161ki pristup, radijaciona terapija kao i hemoterapija.<\/p>\n<p>Hirurgija je naj\u010de\u0161\u0107e efikasan tretman, koji se fokusira na kompletno uklanjanje tumorske promene kao i le\u010denje lokalnih recidiva tumora i udaljenih metastaza.<\/p>\n<p>Radijaciona terapija je sastavni deo le\u010denja za svaki tumor mekih tkiva (sarkome). Ordinira se preoperativno ili postoperativno. U kombinaciji sa hirur\u0161kom ekscizijom, radijaciona terapija je efikasna u velikoj meri.<\/p>\n<p>Hemoterapija mo\u017ee tako\u0111e biti preoperativna ili postoperativna. S obzirom na ne\u017eeljene efekte, odluka za le\u010denje tumora primenom hemoterapije trebalo bi biti pa\u017eljivo razmotrena uzimaju\u0107i u obzir individualne karakteriste tumorskog procesa. Pozitivan efekat hemoterapije jeste smanjenje tumorske mase. Naj\u010de\u0161\u0107e, ovaj vid le\u010denja preporu\u010den je kod tumora manjih od 8 cm u dijametru i kod pacijenata mla\u0111ih od 65 godina sa o\u010duvanom sr\u010danom funkcijom.<\/p>\n","protected":false},"featured_media":0,"template":"","class_list":["post-71458","disease","type-disease","status-publish","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v24.3 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Maligni tumori omota\u010da perifernih nerava - Humanitas.net<\/title>\n<meta name=\"robots\" content=\"noindex, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<meta property=\"og:locale\" content=\"sr_RS\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Maligni tumori omota\u010da perifernih nerava - Humanitas.net\" \/>\n<meta property=\"og:description\" content=\"Definicija Maligni tumori omota\u010da perifernih nerava, ili neurofibrosarkomi, predstavljaju vrstu sarkoma koji poti\u010du iz protektivne vrste nerava koji se \u0161ire iz ki\u010dmene mo\u017edine u druge delove tela. 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