{"id":71122,"date":"2017-11-07T20:32:30","date_gmt":"2017-11-07T20:32:30","guid":{"rendered":"http:\/\/humanitasnet-new.local\/malattie\/kastlemanova-bolest\/"},"modified":"2025-01-13T02:53:32","modified_gmt":"2025-01-13T02:53:32","slug":"kastlemanova-bolest","status":"publish","type":"disease","link":"https:\/\/humanitas-net.humweb.webiz.team\/sr\/diseases\/kastlemanova-bolest\/","title":{"rendered":"Kastlemanova bolest"},"content":{"rendered":"<p>Kastlemanova bolest je retka bolest limfnih \u017elezda i povezanih tkiva koje uklju\u010duje prekomerni rast \u0107elija u limfnom sistemu. Poznat je jo\u0161 i kao hiperplazija velikog limfnog \u010dvora, hiperplazija angiofolikularnog limfnog \u010dvora (AFH) ili limfoproliferativni poreme\u0107aj, \u0161to zna\u010di da postoji abnormalno pove\u0107anje \u0107elija u limfnom sistemu. Iako Kastleman (KB) nije zvani\u010dno kancer, jedan oblik ove bolesti (poznat kao multicentri\u010dni Kastleman) pona\u0161a se veoma sli\u010dno limfomu i mnogi ljudi na kraju i dobiju limfom. Stoga se \u010desto le\u010di hemoterapijom ili radioterapijom.<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"simptomi\">Simptomi<\/h2>\n<p>Najbolji na\u010din da se klasifikuje KB je da se utvrdi koliki deo tela je zahva\u0107en jer se slu\u010dajevi razlikuju me\u0111u ljudima. Dva glavna obilka KB su:<\/p>\n<p>Lokalizovani (unicentri\u010dni) gde je zahva\u0107ena samo jednba \u017elezda limfnog sistema; i<\/p>\n<p>Multicentri\u010dni , gde je zahva\u0107eno vi\u0161e limfnih \u010dvorova i limfnih tkiva \u0161to mo\u017ee umnogome oslabitii imuni sistem.<\/p>\n<p>Mnogi ljudi sa KB nemaju nikakve znakle ili simptome bolesti. Oboleli limfni \u010dvor se obi\u010dno nalazi u grudima, vratu ili stomaku. Kada su simptomi i znaci prisutni, oni mogu uklju\u010diti:<\/p>\n<p>Ose\u0107aj teskobe i pritiska u grudima ili stomaku koje izazivaju te\u0161ko\u0107e u disanju i ishrani;<\/p>\n<p>Uve\u0107ana grudvica ispod ko\u017ee u predelu vrata, prepona ili pazuha;<\/p>\n<p>Nenamerni gubitak te\u017eine<\/p>\n<p>Ne tako \u010desto, groznica, no\u0107no znojenje i slabost.<\/p>\n<p>Mnogi ljudi sa multicentri\u010dnim KB imaju temperaturu, no\u0107no znojenje, umor i slabost, gubitak apetita, nenamerni gubitak te\u017eine, uve\u0107ane limfne \u010dvorove i jetru ili slezinu.<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"uzroci\">Uzroci<\/h2>\n<p>Nije potpuno jasno koji su ta\u010dni uzroci KB. Me\u0111utim, infekcija virusom herpes 8 (HHV-8) povezuje se sa multicentri\u010dnim tipom KB. Ta\u010dna uloga HHV-8 jo\u010d uvek nije jasna, ali izgleda da izaziva brzo stvarane novih \u0107elija imunog sistema. \u0106elije imunog sistema proizvode protein koji se zove interleukin-6 koji potpoma\u017ee rast limfnih \u0107elija.<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"komplikacije\">Komplikacije<\/h2>\n<p>Ljudi sa unicentri\u010dnom KB se obi\u010dno ose\u0107aju dobro kada je uklonjen zahva\u0107eni limfni \u010dvor. Me\u0111utim, ako imate KB, to mo\u017ee pove\u0107ati rizik od limfoma.<\/p>\n<p>Krajnji ishod za ljude sa multicentri\u010dnom KB varira, u zavisnosti od prirode bolesti. Komplikacije kod multicentri\u010dne KB mogu biti opasne po \u017eivot i uklju\u010duju:<\/p>\n<p>Infekcije koje dovode do otkazivanja mnogih organa<\/p>\n<p>Kancer, kao \u0161to je limfom ili Kaposijev sarkom<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"faktori-rizika\">Faktori rizika<\/h2>\n<p>KB se mo\u017ee javiti kod bilo koga, ali prose\u010dne godine u kojima se javlja je 35. Najve\u0107i broj ljudi sa multicentri\u010dnim oblikom su stariji (u 50im i 60im godinama). Multicentri\u010dni oblik je tako\u0111e \u010de\u0161\u0107i kod mu\u0161karaca nego kod \u017eena.<\/p>\n","protected":false},"featured_media":0,"template":"","class_list":["post-71122","disease","type-disease","status-publish","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v24.3 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Kastlemanova bolest - Humanitas.net<\/title>\n<meta name=\"robots\" content=\"noindex, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<meta property=\"og:locale\" content=\"sr_RS\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Kastlemanova bolest - Humanitas.net\" \/>\n<meta property=\"og:description\" content=\"Kastlemanova bolest je retka bolest limfnih \u017elezda i povezanih tkiva koje uklju\u010duje prekomerni rast \u0107elija u limfnom sistemu. Poznat je jo\u0161 i kao hiperplazija velikog limfnog \u010dvora, hiperplazija angiofolikularnog limfnog \u010dvora (AFH) ili limfoproliferativni poreme\u0107aj, \u0161to zna\u010di da postoji abnormalno pove\u0107anje \u0107elija u limfnom sistemu. 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