{"id":72969,"date":"2020-10-29T10:56:44","date_gmt":"2020-10-29T10:56:44","guid":{"rendered":"http:\/\/humanitasnet-new.local\/malattie\/rabdomiosarkom-2\/"},"modified":"2025-01-13T03:19:54","modified_gmt":"2025-01-13T03:19:54","slug":"rabdomiosarkom","status":"publish","type":"disease","link":"https:\/\/humanitas-net.humweb.webiz.team\/sl\/diseases\/rabdomiosarkom\/","title":{"rendered":"Rabdomiosarkom"},"content":{"rendered":"<h2 id=\"opredelitev\">Opredelitev<\/h2>\n<p>Rabdomiosarkom je rakavi tumor mi\u0161ic, ki so pritrjene na kosti. Medtem ko se rak lahko pojavi na \u0161tevilnih predelih telesa, najpogostej\u0161a mesta RMS vklju\u010dujejo glavo in vrat, se\u010dne in reproduktivne organe, roke, noge in prtlja\u017enik. Ker je rabdomiosarkom rak embrionalnih celic, je pri otrocih veliko pogostej\u0161i, \u010deprav se lahko v\u010dasih pojavi tudi pri odraslih.<\/p>\n<p>Obstajata dve glavni vrsti RMS: embrionalni rabdomiosarkom in alveolarni rabdomiosarkom.<\/p>\n<p>\u00d8 Embrionalni rabdomiosarkom je pogost rak, ki se obi\u010dajno razvije pri otrocih do 5. leta starosti na dolo\u010denih podro\u010djih, kot so glava in vrat, mehur, no\u017enica, v prostati ali v testisih.<\/p>\n<p>\u00d8 Alveolarni rabdomiosarkom je rak, ki obi\u010dajno prizadene vse starostne skupine in se najpogosteje razvije v velikih mi\u0161icah trupa, rok in nog.<\/p>\n<p>Mo\u017enosti zdravljenja rabdomiosarkoma obi\u010dajno vklju\u010dujejo kirur\u0161ki poseg, pa tudi obsevanje ali kemoterapijo.<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"simptomi\">Simptomi<\/h2>\n<p>Simptomi rabdomiosarkoma so obi\u010dajno odvisni od lokacije tumorja, njegove velikosti in od tega, ali se je raz\u0161iril na druga podro\u010dja telesa. Najpogostej\u0161i simptom vklju\u010duje gnoj, ki lahko ali ne bo bole\u010d.<\/p>\n<p>Tumorji v nosu: krvavitev, te\u017eave pri po\u017eiranju, zastoji<\/p>\n<p>Tumorji okoli o\u010di: izboklina o\u010desa, oslabljen vid, vnetje ali bole\u010dina okoli o\u010desa<\/p>\n<p>Tumorji v u\u0161esih: u\u0161esni u\u0161es, izguba sluha, vnetje<\/p>\n<p>Tumorji v trebuhu: bole\u010dine v trebuhu, bruhanje, zaprtje<\/p>\n<p>Tumorji v mehurju ali vagini: kri v urinu, vaginalna krvavitev<\/p>\n<p>\u010ce RMS napreduje, lahko povzro\u010di huj\u0161e simptome, kot so bule pod ko\u017eo, bole\u010dine v kosteh, kroni\u010dni ka\u0161elj, \u0161ibkost ali izguba te\u017ee.<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"vzroki\">Vzroki<\/h2>\n<p>Natan\u010den vzrok rabdomiosarkoma \u0161e vedno ni znan. Raziskovalci verjamejo, da spremembe genov lahko vodijo do RMS, \u010deprav ni jasno, kaj povzro\u010da spremembe. Nekatere spremembe genov se lahko podedujejo, druge pa so lahko samo naklju\u010dni primeri, ki se zgodijo znotraj celic (to\u010dka, ko normalne celice postanejo rakave celice).<\/p>\n<p>Ni sprememba \u017eivljenjskega sloga ali okoljski vzrok, ki bi lahko spremenil pojav RMS, zato prepre\u010devanje raka ni verjetno.<\/p>\n<h2 id=\"dejavniki-tveganja\">Dejavniki tveganja<\/h2>\n<p>Nekaj \u200b\u200bdejavnikov, ki lahko pove\u010dajo tveganje za razvoj rabdomiosarkoma, vklju\u010duje naslednje:<\/p>\n<ul>\n<li>\u010ce smo otrok, mlaj\u0161i od 10 let<\/li>\n<li>Mo\u0161ki spol<\/li>\n<li>Dolo\u010dena podedovana stanja (Nevrofibromatoza tip 1, Costello sindrom, Noonanov sindrom)<\/li>\n<li>Izpostavljenost rentgenom pred rojstvom<\/li>\n<\/ul>\n<h2 id=\"\"><\/h2>\n<h2 id=\"zapleti\">Zapleti<\/h2>\n<p>Nekaj \u200b\u200bzapletov, ki lahko izhajajo iz rabdomiosarkoma, vklju\u010duje naslednje:<\/p>\n<ul>\n<li>Zapleti zaradi kemoterapije<\/li>\n<li>Nezmo\u017enost operacije zaradi lokacije tumorja<\/li>\n<li>\u0160irjenje raka na druga podro\u010dja telesa<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n<h2 id=\"zdravljenje\">Zdravljenje<\/h2>\n<p>Mo\u017enosti zdravljenja rabdomiosarkoma so obi\u010dajno odvisne od lokacije tumorja, njegove velikosti in vrste rabdomiosarkoma, za katerim posameznik trpi. Pomembno je, da bolniki, ki jim je diagnosticiran rabdomiosarkom, razumejo mo\u017ene stranske u\u010dinke zdravljenja raka in v kak\u0161nem obsegu se lahko zdravljenje izka\u017ee za uspe\u0161no. Mo\u017enosti zdravljenja lahko vklju\u010dujejo:<\/p>\n<ul>\n<li>Kirur\u0161ki poseg: kirur\u0161ki poseg, ki vklju\u010duje odstranitev tumorja.<\/li>\n<li>Sevalna terapija: vrsta terapije, ki vklju\u010duje uporabo mo\u010dnih rentgenskih \u017earkov za ubijanje rakavih celic.<\/li>\n<li>Kemoterapija: vrsta terapije, ki vklju\u010duje uporabo kemi\u010dnih snovi (protirakavih zdravil) za uni\u010denje rakavih celic in prepre\u010devanje nadaljnjega \u0161irjenja raka.<\/li>\n<\/ul>\n","protected":false},"featured_media":0,"template":"","class_list":["post-72969","disease","type-disease","status-publish","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v24.3 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Rabdomiosarkom - Humanitas.net<\/title>\n<meta name=\"robots\" content=\"noindex, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<meta property=\"og:locale\" content=\"sl_SI\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Rabdomiosarkom - Humanitas.net\" \/>\n<meta property=\"og:description\" content=\"Opredelitev Rabdomiosarkom je rakavi tumor mi\u0161ic, ki so pritrjene na kosti. 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Medtem ko se rak lahko pojavi na \u0161tevilnih predelih telesa, najpogostej\u0161a mesta RMS vklju\u010dujejo glavo in vrat, se\u010dne in reproduktivne organe, roke, noge in prtlja\u017enik. Ker je rabdomiosarkom rak embrionalnih celic, je pri otrocih veliko pogostej\u0161i, \u010deprav se lahko v\u010dasih pojavi tudi pri odraslih. 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