{"id":72933,"date":"2020-11-03T10:38:29","date_gmt":"2020-11-03T10:38:29","guid":{"rendered":"http:\/\/humanitasnet-new.local\/malattie\/pectus-carinatum-3\/"},"modified":"2025-01-13T03:19:24","modified_gmt":"2025-01-13T03:19:24","slug":"pectus-carinatum","status":"publish","type":"disease","link":"https:\/\/humanitas-net.humweb.webiz.team\/sl\/diseases\/pectus-carinatum\/","title":{"rendered":"Pectus carinatum"},"content":{"rendered":"<h2 id=\"opredelitev\">Opredelitev<\/h2>\n<p>Pectus carinatum je redka prirojena napaka, ki vklju\u010duje deformacijo prsnega ko\u0161a. Upodobljen je z nenormalno navzven obrnjeno izboklino prsnice in reber. V nekaterih primerih je deformacija opazna \u0161ele po tem, ko mladostnik odraste. \u010ceprav pektus karinatum v\u010dasih moti splo\u0161no zdravje posameznika, ve\u010dina posameznikov na splo\u0161no razvije normalno delovanje srca in plju\u010d.<\/p>\n<p>V ve\u010dini primerov otrok in mladih z pektusnim karinatumom je najve\u010dji izziv \u017eivljenje z deformiteto. Oblika prsnega ko\u0161a lahko \u0161koduje posameznikovi samopodobi in samozavesti, kar posledi\u010dno pomeni socialni umik.<\/p>\n<p>Priporo\u010dena mo\u017enost zdravljenja za otroke, ki trpijo zaradi pektusov karinatum, je da nosijo naramnico, ki lahko pomaga splo\u0161\u010diti prsni ko\u0161 in prepre\u010diti poseganje v rasto\u010de kosti. V primerih hudega pektusnega karinatuma je priporo\u010dljiva kirur\u0161ka sanacija.<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"simptomi\">Simptomi<\/h2>\n<p>Znaki in simptomi pektus carinatum vklju\u010dujejo:<\/p>\n<ul>\n<li>Zunanji polo\u017eaj prsne stene<\/li>\n<li>Bole\u010dina in ob\u010dutljivost na obmo\u010dju zara\u0161\u010denih hrustancev<\/li>\n<li>Zasoplost<\/li>\n<li>Utrujenost<\/li>\n<li>Blaga do zmerna astma<\/li>\n<li>Psiholo\u0161ke spremembe (nihanje razpolo\u017eenja, ob\u010dutek nelagodja na ko\u017ei, socialni umik)<\/li>\n<\/ul>\n<h2 id=\"vzroki\">Vzroki<\/h2>\n<p>\u010ceprav natan\u010den vzrok \u0161e vedno ostaja neznan, se pektus carinatum ponavadi ponovi v dru\u017einah, kar nakazuje, da lahko genetika igra pomembno vlogo. To je posledica prirojene napake, ko hrustanec zaraste, kar posledi\u010dno povzro\u010di, da prsnica \u0161trli naprej. Pektus karinatum se lahko pojavi kot posamezna in lo\u010dena nepravilnost ali v povezavi z drugimi genetskimi motnjami ali sindromi. Ti sindromi lahko vklju\u010dujejo:<\/p>\n<ul>\n<li>Turnerjev sindrom<\/li>\n<li>Noonanov sindrom<\/li>\n<li>Marfanov sindrom<\/li>\n<li>Ehlers-Danlos sindrom<\/li>\n<li>Morquio sindrom<\/li>\n<li>Sindrom ve\u010d lentiginov<\/li>\n<li>Sly sindrom<\/li>\n<li>Skolioza<\/li>\n<li>Trisomija 18<\/li>\n<li>Trisomija 21<\/li>\n<li>Osteogeneza je nepopolna<\/li>\n<li>Homocistinurija<\/li>\n<\/ul>\n<h2 id=\"zdravljenje\">Zdravljenje<\/h2>\n<p>Mo\u017enosti zdravljenja Pectus carinatum so obi\u010dajno odvisne od starosti posameznika, njihovega splo\u0161nega zdravstvenega stanja in splo\u0161ne resnosti njihovega stanja.<\/p>\n<p>Pri otrocih do 18. leta, ki imajo blag do zmeren pektus karinatum, je priporo\u010dena mo\u017enost zdravljenja krepitev prsne stene.<\/p>\n<p>&nbsp;<\/p>\n<ul>\n<li>Okrepitev: Postopek, ki vklju\u010duje prilagajanje zunanje obodne opornice po meri, ki usmerja pritisk na prsnico ali hrustanec, da se splo\u0161\u010di stena prsnega ko\u0161a. Ko otrok raste in se izbolj\u0161a pektus, bodo morda potrebne prilagoditve. Opornico je treba nositi ves dan in no\u010d, za zagotovitev pozitivnih kon\u010dnih rezultatov pa je potreben reden nadzor.<\/li>\n<\/ul>\n<p>Pri osebah s hudim pektusnim karinatumom se lahko priporo\u010di operacija kot mo\u017enost zdravljenja.<\/p>\n<ul>\n<li>Ravitch tehnika: kirur\u0161ki postopek, ki vklju\u010duje rez na prsih, odstranitev nenormalnega hrustanca in odvajanje prsnice. Pod prsnico se poleg tega vstavi majhen drog, da se hrbet dr\u017ei v ustreznem polo\u017eaju, dokler hrustanec ne zraste nazaj, v povpre\u010dju pribli\u017eno 6 mesecev.<\/li>\n<li>Nussova tehnika: Manj invaziven kirur\u0161ki poseg, ki vklju\u010duje postavitev ene ali ve\u010d konkavnih jeklenih palic v prsni ko\u0161, pod prsnico. Palica je nastavljena tako, da se potisne navznoter na prsnico, da se popravi deformacija. Palica obi\u010dajno ostane v telesu pribli\u017eno dve leti, dokler se kosti ne strdijo.<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n<p>Po adolescenci lahko nekateri izberejo bodybuilding kot na\u010din za prikrivanje deformacije. Bodybuilding se priporo\u010da posameznikom s simetri\u010dnim pektusnim karinatumom.<\/p>\n","protected":false},"featured_media":0,"template":"","class_list":["post-72933","disease","type-disease","status-publish","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v24.3 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Pectus carinatum - Humanitas.net<\/title>\n<meta name=\"robots\" content=\"noindex, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<meta property=\"og:locale\" content=\"sl_SI\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Pectus carinatum - Humanitas.net\" \/>\n<meta property=\"og:description\" content=\"Opredelitev Pectus carinatum je redka prirojena napaka, ki vklju\u010duje deformacijo prsnega ko\u0161a. Upodobljen je z nenormalno navzven obrnjeno izboklino prsnice in reber. V nekaterih primerih je deformacija opazna \u0161ele po tem, ko mladostnik odraste. \u010ceprav pektus karinatum v\u010dasih moti splo\u0161no zdravje posameznika, ve\u010dina posameznikov na splo\u0161no razvije normalno delovanje srca in plju\u010d. 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