{"id":72891,"date":"2020-11-03T13:29:28","date_gmt":"2020-11-03T13:29:28","guid":{"rendered":"http:\/\/humanitasnet-new.local\/malattie\/moyamoya-bolezen\/"},"modified":"2025-01-13T03:18:49","modified_gmt":"2025-01-13T03:18:49","slug":"moyamoya-bolezen","status":"publish","type":"disease","link":"https:\/\/humanitas-net.humweb.webiz.team\/sl\/diseases\/moyamoya-bolezen\/","title":{"rendered":"Moyamoya bolezen"},"content":{"rendered":"<h2 id=\"opredelitev\">Opredelitev<\/h2>\n<p>Bolezen Moyamoya je redka, a progresivna mo\u017egansko \u017eilna motnja. Nastane, ko so dolo\u010dene arterije v mo\u017eganih zo\u017eene. Zo\u017eenje, pa tudi krvni strdki, blokirajo pretok krvi v mo\u017egane. Nato nastanejo zapleteni drobni kolateralni posodi okoli blokiranih plovil, ki nadomestijo blokado. Nastala \u017eila so majhna in \u0161ibka in se na rentgenskem slikanju ka\u017eejo kot &#8220;dim dima&#8221;.<\/p>\n<p>Bolezen najpogosteje prizadene otroke, pojavlja pa se lahko tudi pri odraslih. Prvi simptom zdravila Moyamoya pri otrocih je ponavadi mo\u017eganska kap ali ponavljajo\u010di se prehodni ishemi\u010dni napadi, ki jih pogosto imenujemo &#8220;mini udarci&#8221;. Drugi spremljajo\u010di simptomi so napadi in \u0161ibkost mi\u0161ic, prav tako lahko postane paralizirana ena stran telesa. Odrasli imajo obi\u010dajno hemoragi\u010dno kap zaradi krvnih strdkov, ki se ponovno pojavijo v prizadetih mo\u017eganskih \u017eilah. Nekateri ljudje lahko ob\u010dutijo pomanjkanje zavesti, pomanjkanje govora, oslabljene senzori\u010dne in kognitivne sposobnosti, te\u017eave z vidom in nenamerno gibanje.<\/p>\n<p>Raziskovalci verjamejo, da se bolezen Moyamoya pojavi kot posledica podedovanih genetskih nepravilnosti.<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"simptomi\">Simptomi<\/h2>\n<p>Nekateri naslednji simptomi se lahko pojavijo pri otrocih in odraslih:<\/p>\n<ul>\n<li>Kap<\/li>\n<li>Epilepti\u010dni napadi<\/li>\n<li>Mi\u0161i\u010dna \u0161ibkost<\/li>\n<li>Paralizirana ena stran telesa<\/li>\n<li>Hemoragi\u010dna kap<\/li>\n<li>Motena zavest<\/li>\n<li>Govorni primanjkljaji (afazija)<\/li>\n<li>Slaba senzorika<\/li>\n<li>Kognitivne okvare<\/li>\n<li>Te\u017eave z vidom<\/li>\n<li>Neprostovoljno gibanje<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"zdravljenje\">Zdravljenje<\/h2>\n<p>Zdravljenje bolezni Moyamoya je obi\u010dajno operativni poseg. Postopek se imenuje revaskularizacijska kirurgija, med katero se obnovi dotok krvi v mo\u017egane z odpiranjem zo\u017eenih krvnih \u017eil ali z obhodom blokiranih arterij. Otroci imajo ponavadi bolj\u0161i rezultat operacije kot odrasli, vendar ve\u010dina bolnikov, ki jim je bila podvr\u017eena tovrstna operacija, po posegu ne do\u017eivi mo\u017eganske kapi ali drugih povezanih te\u017eav.<\/p>\n<p>&nbsp;<\/p>\n","protected":false},"featured_media":0,"template":"","class_list":["post-72891","disease","type-disease","status-publish","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v24.3 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Moyamoya bolezen - Humanitas.net<\/title>\n<meta name=\"robots\" content=\"noindex, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<meta property=\"og:locale\" content=\"sl_SI\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Moyamoya bolezen - Humanitas.net\" \/>\n<meta property=\"og:description\" content=\"Opredelitev Bolezen Moyamoya je redka, a progresivna mo\u017egansko \u017eilna motnja. 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