{"id":72875,"date":"2020-11-03T13:37:28","date_gmt":"2020-11-03T13:37:28","guid":{"rendered":"http:\/\/humanitasnet-new.local\/malattie\/maligni-tumorji-obodnih-zivcnih-ovojnic\/"},"modified":"2025-01-13T03:18:36","modified_gmt":"2025-01-13T03:18:36","slug":"maligni-tumorji-obodnih-zivcnih-ovojnic","status":"publish","type":"disease","link":"https:\/\/humanitas-net.humweb.webiz.team\/sl\/diseases\/maligni-tumorji-obodnih-zivcnih-ovojnic\/","title":{"rendered":"Maligni tumorji obodnih \u017eiv\u010dnih ovojnic"},"content":{"rendered":"<h2 id=\"opredelitev\">Opredelitev<\/h2>\n<p>Maligni tumorji obodnih obodnih \u017eivcev ali tudi nevrofibrosarkomi so neke vrste sarkomi, ki izvirajo iz za\u0161\u010ditne linije \u017eivcev, ki se \u0161irijo iz hrbtenja\u010de v telo. Pojavijo se lahko kjer koli v telesu, vendar najpogosteje primere tak\u0161nih tumorjev najdemo v globokem tkivu rok, nog in trupa. Povzro\u010dajo bole\u010dino in \u0161ibkost, v\u010dasih tudi kepico. Ti tumorji so pogostej\u0161i pri ljudeh, ki imajo dedno nagnjenost k razvoju \u017eiv\u010dnih tumorjev, in pri ljudeh, ki so \u017ee imeli terapijo za zdravljenje raka. Vendar pa mnogi ljudje, ki trpijo zaradi malignih tumorjev obodnih \u017eiv\u010dnih ovojnic, nimajo nobenih dejavnikov tveganja. Tovrstne tumorje zdravimo le s kirur\u0161kim posegom, \u010demur sledijo kemoterapija in radioterapija.<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"simptomi\">Simptomi<\/h2>\n<p>Simptomi lahko vklju\u010dujejo:<\/p>\n<ul>\n<li>Nevrolo\u0161ki simptomi<\/li>\n<li>Bole\u010dina na obmo\u010dju, kjer je tumor lokaliziran<\/li>\n<li>Otekanje v rokah ali nogah (obi\u010dajno nebole\u010de)<\/li>\n<li>Te\u017eave s premikanjem prizadetih okon\u010din<\/li>\n<li>Bole\u010dina<\/li>\n<li>Nelagodje<\/li>\n<li>Otrplost<\/li>\n<li>Izgorevanje<\/li>\n<li>Omoti\u010dnost<\/li>\n<li>Izguba ravnote\u017eja<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n<h2 id=\"vzroki\">Vzroki<\/h2>\n<p>Menijo, da je nevrofibrosarkom lahko genetski, ker so ga odkrili znotraj dru\u017ein. P53 je gen, ki zavira tumor. Menijo, da je genom p53 na 17p pri bolnikih z nevrofibrosarkomom mutiran, kar pove\u010duje verjetnost razvoja raka. Ljudje z inaktiviranim p53 genom nimajo obi\u010dajnega gena p53, ki bi urejal rast celic in zaviral kakr\u0161no koli nenadzorovano rast celic pri zdravi populaciji, zato so \u0161e bolj dovzetni za tumorje. Natan\u010den vzrok pa \u0161e vedno ni znan.<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"zdravljenje\">Zdravljenje<\/h2>\n<p>Mo\u017enosti zdravljenja malignih tumorjev obodnih \u017eiv\u010dnih ovojnic so operacija, radioterapija in kemoterapija.<\/p>\n<p>Obi\u010dajno je kirurgija naju\u010dinkovitej\u0161e zdravljenje, ki se osredoto\u010da na popolno odstranitev tumorja, pa tudi na zdravljenje lokalnih ponovitev tumorjev in oddaljenih metastaz.<\/p>\n<p>Sevalna terapija je obi\u010dajno sestavni del terapij za skoraj vse mehke tkivne sarkome. Lahko se predpi\u0161e predoperativno ali pooperativno. V kombinaciji s kirur\u0161ko ekscizijo je bila sevalna terapija precej u\u010dinkovita.<\/p>\n<p>Kemoterapija je lahko tudi predoperativno ali pooperativno zdravljenje. Ker ima stranske u\u010dinke, je treba skrbno razmisliti o odlo\u010ditvi za zdravljenje tumorja s kemoterapijo, pri \u010demer se upo\u0161tevajo individualne pacientove \u017eelje. Koristi od kemoterapije je mo\u017eno kr\u010denje tumorja. Obi\u010dajno je tak\u0161no zdravljenje priporo\u010dljivo, kadar je tumor premera manj kot 8 cm in kadar bolniki niso starej\u0161i od 65 let z dobrim sr\u010dnim delovanjem.<\/p>\n<p>&nbsp;<\/p>\n","protected":false},"featured_media":0,"template":"","class_list":["post-72875","disease","type-disease","status-publish","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v24.3 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Maligni tumorji obodnih \u017eiv\u010dnih ovojnic - Humanitas.net<\/title>\n<meta name=\"robots\" content=\"noindex, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<meta property=\"og:locale\" content=\"sl_SI\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Maligni tumorji obodnih \u017eiv\u010dnih ovojnic - Humanitas.net\" \/>\n<meta property=\"og:description\" content=\"Opredelitev Maligni tumorji obodnih obodnih \u017eivcev ali tudi nevrofibrosarkomi so neke vrste sarkomi, ki izvirajo iz za\u0161\u010ditne linije \u017eivcev, ki se \u0161irijo iz hrbtenja\u010de v telo. Pojavijo se lahko kjer koli v telesu, vendar najpogosteje primere tak\u0161nih tumorjev najdemo v globokem tkivu rok, nog in trupa. Povzro\u010dajo bole\u010dino in \u0161ibkost, v\u010dasih tudi kepico. 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