{"id":72831,"date":"2020-11-03T15:18:02","date_gmt":"2020-11-03T15:18:02","guid":{"rendered":"http:\/\/humanitasnet-new.local\/malattie\/sindrom-hipoplasticnega-levega-srca\/"},"modified":"2025-01-13T03:17:59","modified_gmt":"2025-01-13T03:17:59","slug":"sindrom-hipoplasticnega-levega-srca","status":"publish","type":"disease","link":"https:\/\/humanitas-net.humweb.webiz.team\/sl\/diseases\/sindrom-hipoplasticnega-levega-srca\/","title":{"rendered":"Sindrom hipoplasti\u010dnega levega srca"},"content":{"rendered":"<p>Sindrom hipoplasti\u010dnega levega srca je redka, a zapletena prirojena sr\u010dna napaka. V tem stanju je leva stran srca kriti\u010dno nerazvita.<\/p>\n<p>Pri hipoplasti\u010dnem sindromu levega srca leva stran srca ne more u\u010dinkovito \u010drpati krvi v telo, zato desna stran srca \u010drpa kri tako v plju\u010da kot tudi po telesu.<\/p>\n<p>Zdravljenje hipoplasti\u010dnega sindroma levega srca vklju\u010duje zdravila, ki prepre\u010dujejo zapiranje povezave (arteriosus kanalov) med desno in levo stranjo ter operacijo ali presaditev srca.<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"simptomi\">Simptomi<\/h2>\n<p>Simptomi hipoplasti\u010dnega sindroma levega srca pri dojen\u010dkih vklju\u010dujejo:<\/p>\n<p>&nbsp;<\/p>\n<ul>\n<li>Sivkasto modra barva ko\u017ee (cianoza)<\/li>\n<li>Hitro, te\u017eko dihanje<\/li>\n<li>Slabo hranjenje<\/li>\n<li>Hladne roke in noge<\/li>\n<li>Nenavadno zaspani ali neaktivni<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n<p>Pri dojen\u010dku s hipoplasti\u010dnim sindromom levega srca, \u010de se naravne povezave med levo in desno stranjo srca zaprejo, lahko dojen\u010dek zaide v \u0161ok in umre. Simptomi \u0161oka vklju\u010dujejo:<\/p>\n<p>&nbsp;<\/p>\n<ul>\n<li>Hladna, lepljiva ko\u017ea (bleda ali siva)<\/li>\n<li>\u0160ibek in hiter utrip<\/li>\n<li>Nenormalno dihanje (po\u010dasno in plitvo ali hitro)<\/li>\n<li>Dilatirani zenici<\/li>\n<li>O\u010di, ki so videti zrele<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n<h2 id=\"vzroki\">Vzroki<\/h2>\n<p>Sindrom hipoplasti\u010dnega levega srca se razvije med rastjo ploda, medtem ko se razvija otrokovo srce. Natan\u010den vzrok pa ni znan.<\/p>\n<p>Pri hipoplasti\u010dnem sindromu levega srca leva stran srca ne more pravilno dovajati krvi, ker je levi prekat premajhen ali pa morda ne obstaja. Poleg tega zaklopke na levi strani srca (aortna in mitralna zaklopka) ne delujejo pravilno in glavna arterija, ki zapu\u0161\u010da srce (aorto), je nenormalno majhna.<\/p>\n<p>V prvih nekaj dneh \u017eivljenja lahko desna stran srca \u010drpa kri tako v plju\u010da kot v preostali del telesa skozi naravno odprtino med zgornjimi prekati srca ali prek krvne \u017eile, ki povezuje plju\u010dno arterijo z aorta. \u010ce pa se te odprtine zaprejo, kar se obi\u010dajno pojavi po prvih nekaj dneh, desna stran ne more \u010drpati krvi v telo.<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"dejavniki-tveganja\">Dejavniki tveganja<\/h2>\n<p>Dru\u017einska anamneza hipoplasti\u010dnega sindroma levega srca pove\u010duje tveganje, da novi dru\u017einski \u010dlani razvijejo stanje. Otrok s hipoplasti\u010dnim sindromom levega srca pove\u010da tveganje, da bo imel \u0161e enega otroka z enakim stanjem.<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"zapleti\">Zapleti<\/h2>\n<p>Sindrom hipoplasti\u010dnega levega srca je brez kirur\u0161kega posega usoden. \u010ceprav mnogi dojen\u010dki pre\u017eivijo z zdravljenjem, se pri njih ve\u010dina razvije kasneje. Zapleti lahko vklju\u010dujejo:<\/p>\n<p>&nbsp;<\/p>\n<ul>\n<li>Lahko se utrudite med \u0161portom ali vajami<\/li>\n<li>Nenormalnosti sr\u010dnega ritma (aritmije)<\/li>\n<li>Nakup teko\u010dine v plju\u010dih, trebuhu, nogah in stopalih (edem)<\/li>\n<li>Nastajanje krvnih strdkov, ki lahko vodijo do plju\u010dne embolije ali kapi<\/li>\n<li>Te\u017eave v razvoju, povezane z mo\u017egani in \u017eiv\u010dnim sistemom<\/li>\n<li>Potreba po dodatnih operacijah srca ali presaditvi<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n<h2 id=\"zdravljenje\">Zdravljenje<\/h2>\n<p>Zdravljenje hipoplasti\u010dnega sindroma levega srca vklju\u010duje tristopenjski kirur\u0161ki poseg ali presaditev srca.<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"pred-operacijo\">Pred operacijo<\/h2>\n<p>&nbsp;<\/p>\n<p>Zdravila, ki pomagajo raz\u0161iriti krvne \u017eile in ohranjati odprt duktus arteriosus<\/p>\n<p>Pomo\u010d pri dihanju za zagotovitev pravilne dostave kisika<\/p>\n<p>Intravenske teko\u010dine<\/p>\n<p>Atrijska septostomija, da ustvari odprtino med zgornjimi prekati srca (atrijem), \u010de se ovala foramena zapre<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"operacija\">Operacija<\/h2>\n<p>Kirur\u0161ki poseg za odpravljanje hipoplasti\u010dnega sindroma levega srca vklju\u010duje postopek v treh korakih, katerega namen je ustvariti normalen pretok krvi v srce in iz njega ter telesu omogo\u010diti prejemanje krvi, bogate s kisikom.<\/p>\n<p>Druga kirur\u0161ka mo\u017enost je presaditev srca, zlasti kadar so okvare zapletene.<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"nadaljnja-oskrba\">Nadaljnja oskrba<\/h2>\n<p>Po sr\u010dni operaciji ali presaditvi bo dojen\u010dek potreboval vse\u017eivljenjsko nadaljnjo oskrbo, ki vklju\u010duje redno spremljanje in tudi zdravila za uravnavanje delovanja srca.<\/p>\n<p>&nbsp;<\/p>\n","protected":false},"featured_media":0,"template":"","class_list":["post-72831","disease","type-disease","status-publish","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v24.3 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Sindrom hipoplasti\u010dnega levega srca - Humanitas.net<\/title>\n<meta name=\"robots\" content=\"noindex, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<meta property=\"og:locale\" content=\"sl_SI\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Sindrom hipoplasti\u010dnega levega srca - Humanitas.net\" \/>\n<meta property=\"og:description\" content=\"Sindrom hipoplasti\u010dnega levega srca je redka, a zapletena prirojena sr\u010dna napaka. 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