{"id":72802,"date":"2020-11-04T10:10:19","date_gmt":"2020-11-04T10:10:19","guid":{"rendered":"http:\/\/humanitasnet-new.local\/malattie\/hemofilija-2\/"},"modified":"2025-01-13T03:17:35","modified_gmt":"2025-01-13T03:17:35","slug":"hemofilija","status":"publish","type":"disease","link":"https:\/\/humanitas-net.humweb.webiz.team\/sl\/diseases\/hemofilija\/","title":{"rendered":"Hemofilija"},"content":{"rendered":"<p>Hemofilija je redko stanje, pri katerem se kri ne strdi normalno zaradi pomanjkanja beljakovin za strjevanje krvi, ali zaradi pomanjkanja dejavnikov strjevanja. Hemofilija povzro\u010di dalj\u0161e krvavitve po rezu ali po\u0161kodbi; vendar je zelo zaskrbljujo\u010de, ko je krvavitev notranja. Notranje krvavitve lahko po\u0161kodujejo organe in tkiva in so lahko smrtno nevarne.<\/p>\n<p>Hemofilija je genetska motnja, kar pomeni, da je podedovana. Zdravila ni, vendar obstajajo na\u010dini zdravljenja, ki nam lahko pomagajo pri obvladovanju bolezni.<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"simptomi\">Simptomi<\/h2>\n<p>Simptomi hemofilije se razlikujejo glede na raven dejavnikov strjevanja. \u010ce se raven dejavnikov strjevanja nekoliko zmanj\u0161a, lahko pride do krvavitve po operaciji ali po po\u0161kodbi. Na drugi strani pa se lahko pojavijo spontane krvavitve, \u010de imamo hudo pomanjkanje dejavnikov strjevanja.<\/p>\n<p>&nbsp;<\/p>\n<p>Simptomi spontane krvavitve:<\/p>\n<p>&nbsp;<\/p>\n<ul>\n<li>Nepojasnjena in prekomerna krvavitev zaradi ureznin, po\u0161kodb ali po operaciji ali zobozdravstvenem delu<\/li>\n<li>Veliko velikih ali globokih modric<\/li>\n<li>Krvavitve po cepljenju<\/li>\n<li>Bole\u010dina, oteklina ali tesnost v sklepih<\/li>\n<li>Kri v urinu ali blatu<\/li>\n<li>Nepojasnjene krvavitve iz nosu<\/li>\n<li>Nepojasnjena razdra\u017eljivost pri dojen\u010dkih<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n<p>Nujni simptomi hemofilije:<\/p>\n<p>&nbsp;<\/p>\n<ul>\n<li>Nenadna bole\u010dina, oteklina in toplota v velikih sklepih (koleni, komolci, boki, ramena in okon\u010dine)<\/li>\n<li>Krvavitev zaradi po\u0161kodbe<\/li>\n<li>Bole\u010d podalj\u0161ani glavobol<\/li>\n<li>Ponavljajo\u010de se bruhanje<\/li>\n<li>Izjemna utrujenost<\/li>\n<li>Bole\u010dine v vratu<\/li>\n<li>Dvojni vid<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n<h2>\nVzroki<\/h2>\n<p>Ko pride do krvavitve, telo obi\u010dajno zdru\u017ei krvne celice in ustvari strdek, ki zaustavi krvavitev. Postopek strjevanja spodbujajo dolo\u010deni delci krvi, kot so trombociti in plazemski proteini. Pomanjkanje enega od dejavnikov strjevanja povzro\u010da hemofilijo. Hemofilijo se podeduje; vendar nekateri primeri hemofilije nimajo dru\u017einske anamneze. V teh primerih hemofilijo povzro\u010di spontana genetska mutacija. Obstaja ve\u010d vrst hemofilije, ki so razvr\u0161\u010dene glede na to, kateri dejavnik strjevanja je pomanjkljiv:<\/p>\n<p>Hemofilija A: najpogostej\u0161a vrsta bolezni, ki jo povzro\u010da nezadostni faktor strjevanja VIII.<\/p>\n<p>Hemofilija B: Druga najpogostej\u0161a vrsta, ki jo povzro\u010da nezadostni faktor strjevanja IX.<\/p>\n<p>Hemofilija C: Ta vrsta ima blage simptome, povzro\u010da pa jo nezadostni faktor strjevanja XI.<\/p>\n<p>Dedovanje hemofilije je odvisno od vrste hemofilije:<\/p>\n<p>Hemofilija A ali B: Gen, ki povzro\u010da te vrste bolezni, se nahaja na kromosomu X in se lahko prena\u0161a od matere do sina prek enega od materinih genov. Hemofilija A ali B se pojavlja predvsem pri de\u010dkih, medtem ko so \u017eenske z okvarjenim genom nosilke in ne ka\u017eejo nobenih simptomov. Pri \u017eenskah se lahko pojavijo simptomi, \u010de se dejavniki VIII ali IX nekoliko zmanj\u0161ajo.<\/p>\n<p>Hemofilija C: Tovrstno motnjo lahko otroku preneseta oba star\u0161a in se lahko enakovredno pojavi pri deklicah in de\u010dkih.<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"zapleti\">Zapleti<\/h2>\n<p>Zapleti hemofilije vklju\u010dujejo:<\/p>\n<ul>\n<li>Globoka notranja krvavitev: Globoka krvavitev iz mi\u0161ic lahko povzro\u010di otekanje okon\u010din. Oteklina lahko pritisne na \u017eivce in vodi v otrplost ali bole\u010dino.<\/li>\n<li>Po\u0161kodba sklepov: Notranja krvavitev lahko pritiska na sklepe in povzro\u010di mo\u010dne bole\u010dine. \u010ce se bolezen ne zdravi, pogoste notranje krvavitve lahko privedejo do artritisa ali uni\u010denja sklepa.<\/li>\n<li>Oku\u017eba: Ljudje s hemofilijo imajo ve\u010dje tveganje za oku\u017ebo zaradi onesna\u017eenih krvnih pripravkov med transfuzijami krvi.<\/li>\n<li>Ne\u017eeleni u\u010dinki zdravljenja dejavnika strjevanja: Nekateri ljudje imajo negativno reakcijo na zdravljenje faktorjev strjevanja, zaradi \u010desar imunski sistem razvije zaviralce, ki deaktivirajo dejavnike strjevanja, zaradi \u010desar je zdravljenje manj u\u010dinkovito.<\/li>\n<\/ul>\n","protected":false},"featured_media":0,"template":"","class_list":["post-72802","disease","type-disease","status-publish","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v24.3 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Hemofilija - Humanitas.net<\/title>\n<meta name=\"robots\" content=\"noindex, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<meta property=\"og:locale\" content=\"sl_SI\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Hemofilija - Humanitas.net\" \/>\n<meta property=\"og:description\" content=\"Hemofilija je redko stanje, pri katerem se kri ne strdi normalno zaradi pomanjkanja beljakovin za strjevanje krvi, ali zaradi pomanjkanja dejavnikov strjevanja. Hemofilija povzro\u010di dalj\u0161e krvavitve po rezu ali po\u0161kodbi; vendar je zelo zaskrbljujo\u010de, ko je krvavitev notranja. Notranje krvavitve lahko po\u0161kodujejo organe in tkiva in so lahko smrtno nevarne. Hemofilija je genetska motnja, kar [&hellip;]\" \/>\n<meta property=\"og:url\" content=\"https:\/\/humanitas-net.humweb.webiz.team\/sl\/diseases\/hemofilija\/\" \/>\n<meta property=\"og:site_name\" content=\"Humanitas.net\" \/>\n<meta property=\"article:publisher\" content=\"https:\/\/www.facebook.com\/HumanitasInternational\/\" \/>\n<meta property=\"article:modified_time\" content=\"2025-01-13T03:17:35+00:00\" \/>\n<meta name=\"twitter:card\" content=\"summary_large_image\" \/>\n<meta name=\"twitter:site\" content=\"@humanitasmilano\" \/>\n<meta name=\"twitter:label1\" content=\"Est. reading time\" \/>\n\t<meta name=\"twitter:data1\" content=\"3 minutes\" \/>\n<script type=\"application\/ld+json\" class=\"yoast-schema-graph\">{\"@context\":\"https:\/\/schema.org\",\"@graph\":[{\"@type\":\"WebPage\",\"@id\":\"https:\/\/humanitas-net.humweb.webiz.team\/sl\/diseases\/hemofilija\/\",\"url\":\"https:\/\/humanitas-net.humweb.webiz.team\/sl\/diseases\/hemofilija\/\",\"name\":\"Hemofilija - Humanitas.net\",\"isPartOf\":{\"@id\":\"https:\/\/humanitas-net.humweb.webiz.team\/#website\"},\"datePublished\":\"2020-11-04T10:10:19+00:00\",\"dateModified\":\"2025-01-13T03:17:35+00:00\",\"breadcrumb\":{\"@id\":\"https:\/\/humanitas-net.humweb.webiz.team\/sl\/diseases\/hemofilija\/#breadcrumb\"},\"inLanguage\":\"sl-SI\",\"potentialAction\":[{\"@type\":\"ReadAction\",\"target\":[\"https:\/\/humanitas-net.humweb.webiz.team\/sl\/diseases\/hemofilija\/\"]}]},{\"@type\":\"BreadcrumbList\",\"@id\":\"https:\/\/humanitas-net.humweb.webiz.team\/sl\/diseases\/hemofilija\/#breadcrumb\",\"itemListElement\":[{\"@type\":\"ListItem\",\"position\":1,\"name\":\"Home\",\"item\":\"https:\/\/humanitas-net.humweb.webiz.team\/\"},{\"@type\":\"ListItem\",\"position\":2,\"name\":\"Malattie\",\"item\":\"https:\/\/humanitas-net.humweb.webiz.team\/malattie\/\"},{\"@type\":\"ListItem\",\"position\":3,\"name\":\"Hemofilija\"}]},{\"@type\":\"WebSite\",\"@id\":\"https:\/\/humanitas-net.humweb.webiz.team\/#website\",\"url\":\"https:\/\/humanitas-net.humweb.webiz.team\/\",\"name\":\"Humanitas.net\",\"description\":\"Humanitas Hospital\",\"publisher\":{\"@id\":\"https:\/\/humanitas-net.humweb.webiz.team\/#organization\"},\"potentialAction\":[{\"@type\":\"SearchAction\",\"target\":{\"@type\":\"EntryPoint\",\"urlTemplate\":\"https:\/\/humanitas-net.humweb.webiz.team\/?s={search_term_string}\"},\"query-input\":{\"@type\":\"PropertyValueSpecification\",\"valueRequired\":true,\"valueName\":\"search_term_string\"}}],\"inLanguage\":\"sl-SI\"},{\"@type\":\"Organization\",\"@id\":\"https:\/\/humanitas-net.humweb.webiz.team\/#organization\",\"name\":\"Humanitas\",\"url\":\"https:\/\/humanitas-net.humweb.webiz.team\/\",\"logo\":{\"@type\":\"ImageObject\",\"inLanguage\":\"sl-SI\",\"@id\":\"https:\/\/humanitas-net.humweb.webiz.team\/#\/schema\/logo\/image\/\",\"url\":\"https:\/\/humanitas-net.humweb.webiz.team\/wp-content\/uploads\/2025\/01\/new-humanitas-logo-1.svg\",\"contentUrl\":\"https:\/\/humanitas-net.humweb.webiz.team\/wp-content\/uploads\/2025\/01\/new-humanitas-logo-1.svg\",\"width\":1,\"height\":1,\"caption\":\"Humanitas\"},\"image\":{\"@id\":\"https:\/\/humanitas-net.humweb.webiz.team\/#\/schema\/logo\/image\/\"},\"sameAs\":[\"https:\/\/www.facebook.com\/HumanitasInternational\/\",\"https:\/\/x.com\/humanitasmilano\"]}]}<\/script>\n<!-- \/ Yoast SEO plugin. -->","yoast_head_json":{"title":"Hemofilija - Humanitas.net","robots":{"index":"noindex","follow":"follow","max-snippet":"max-snippet:-1","max-image-preview":"max-image-preview:large","max-video-preview":"max-video-preview:-1"},"og_locale":"sl_SI","og_type":"article","og_title":"Hemofilija - Humanitas.net","og_description":"Hemofilija je redko stanje, pri katerem se kri ne strdi normalno zaradi pomanjkanja beljakovin za strjevanje krvi, ali zaradi pomanjkanja dejavnikov strjevanja. Hemofilija povzro\u010di dalj\u0161e krvavitve po rezu ali po\u0161kodbi; vendar je zelo zaskrbljujo\u010de, ko je krvavitev notranja. Notranje krvavitve lahko po\u0161kodujejo organe in tkiva in so lahko smrtno nevarne. Hemofilija je genetska motnja, kar [&hellip;]","og_url":"https:\/\/humanitas-net.humweb.webiz.team\/sl\/diseases\/hemofilija\/","og_site_name":"Humanitas.net","article_publisher":"https:\/\/www.facebook.com\/HumanitasInternational\/","article_modified_time":"2025-01-13T03:17:35+00:00","twitter_card":"summary_large_image","twitter_site":"@humanitasmilano","twitter_misc":{"Est. reading time":"3 minutes"},"schema":{"@context":"https:\/\/schema.org","@graph":[{"@type":"WebPage","@id":"https:\/\/humanitas-net.humweb.webiz.team\/sl\/diseases\/hemofilija\/","url":"https:\/\/humanitas-net.humweb.webiz.team\/sl\/diseases\/hemofilija\/","name":"Hemofilija - Humanitas.net","isPartOf":{"@id":"https:\/\/humanitas-net.humweb.webiz.team\/#website"},"datePublished":"2020-11-04T10:10:19+00:00","dateModified":"2025-01-13T03:17:35+00:00","breadcrumb":{"@id":"https:\/\/humanitas-net.humweb.webiz.team\/sl\/diseases\/hemofilija\/#breadcrumb"},"inLanguage":"sl-SI","potentialAction":[{"@type":"ReadAction","target":["https:\/\/humanitas-net.humweb.webiz.team\/sl\/diseases\/hemofilija\/"]}]},{"@type":"BreadcrumbList","@id":"https:\/\/humanitas-net.humweb.webiz.team\/sl\/diseases\/hemofilija\/#breadcrumb","itemListElement":[{"@type":"ListItem","position":1,"name":"Home","item":"https:\/\/humanitas-net.humweb.webiz.team\/"},{"@type":"ListItem","position":2,"name":"Malattie","item":"https:\/\/humanitas-net.humweb.webiz.team\/malattie\/"},{"@type":"ListItem","position":3,"name":"Hemofilija"}]},{"@type":"WebSite","@id":"https:\/\/humanitas-net.humweb.webiz.team\/#website","url":"https:\/\/humanitas-net.humweb.webiz.team\/","name":"Humanitas.net","description":"Humanitas Hospital","publisher":{"@id":"https:\/\/humanitas-net.humweb.webiz.team\/#organization"},"potentialAction":[{"@type":"SearchAction","target":{"@type":"EntryPoint","urlTemplate":"https:\/\/humanitas-net.humweb.webiz.team\/?s={search_term_string}"},"query-input":{"@type":"PropertyValueSpecification","valueRequired":true,"valueName":"search_term_string"}}],"inLanguage":"sl-SI"},{"@type":"Organization","@id":"https:\/\/humanitas-net.humweb.webiz.team\/#organization","name":"Humanitas","url":"https:\/\/humanitas-net.humweb.webiz.team\/","logo":{"@type":"ImageObject","inLanguage":"sl-SI","@id":"https:\/\/humanitas-net.humweb.webiz.team\/#\/schema\/logo\/image\/","url":"https:\/\/humanitas-net.humweb.webiz.team\/wp-content\/uploads\/2025\/01\/new-humanitas-logo-1.svg","contentUrl":"https:\/\/humanitas-net.humweb.webiz.team\/wp-content\/uploads\/2025\/01\/new-humanitas-logo-1.svg","width":1,"height":1,"caption":"Humanitas"},"image":{"@id":"https:\/\/humanitas-net.humweb.webiz.team\/#\/schema\/logo\/image\/"},"sameAs":["https:\/\/www.facebook.com\/HumanitasInternational\/","https:\/\/x.com\/humanitasmilano"]}]}},"acf":[],"_links":{"self":[{"href":"https:\/\/humanitas-net.humweb.webiz.team\/sl\/wp-json\/wp\/v2\/disease\/72802","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/humanitas-net.humweb.webiz.team\/sl\/wp-json\/wp\/v2\/disease"}],"about":[{"href":"https:\/\/humanitas-net.humweb.webiz.team\/sl\/wp-json\/wp\/v2\/types\/disease"}],"wp:attachment":[{"href":"https:\/\/humanitas-net.humweb.webiz.team\/sl\/wp-json\/wp\/v2\/media?parent=72802"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}