{"id":72768,"date":"2020-11-04T10:15:00","date_gmt":"2020-11-04T10:15:00","guid":{"rendered":"http:\/\/humanitasnet-new.local\/malattie\/fibrozna-displazija-2\/"},"modified":"2025-01-13T03:17:08","modified_gmt":"2025-01-13T03:17:08","slug":"fibrozna-displazija","status":"publish","type":"disease","link":"https:\/\/humanitas-net.humweb.webiz.team\/sl\/diseases\/fibrozna-displazija\/","title":{"rendered":"Fibrozna displazija"},"content":{"rendered":"<p>Fibrozna displazija je redka motnja kosti, pri kateri se namesto normalne kosti razvije brazgotinasto tkivo (fibrozno). To lahko oslabi kost in povzro\u010di, da se kost deformira ali po\u010di.<\/p>\n<p>V ve\u010dini primerov fibrozna displazija vpliva na samo eno kost (najpogosteje lobanjo ali dolgo kost v rokah ali nogah). Ljudje, ki imajo prizadeto ve\u010d kot eno kost, ponavadi razvijejo simptome pred 10-im letom starosti.<\/p>\n<p>Fibrozna displazija je genska motnja in za njo ne obstaja zdravilo. Zdravljenje je fokusirano na olaj\u0161anje simptomov in lahko vklju\u010duje operacijo.<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"simptomi\">Simptomi<\/h2>\n<p>Fibrozna displazija lahko povzro\u010di nekaj ali sploh nobenega od simptomov, \u0161e posebej \u010de gre za bla\u017ejo obliko motnje. Huda fibrozna displazija lahko povzro\u010di naslednje simptome:<\/p>\n<p>&nbsp;<\/p>\n<ul>\n<li>Bole\u010dino v kosteh<\/li>\n<li>Deformacije kosti<\/li>\n<li>Zlomljene kosti<\/li>\n<li>Ukle\u0161\u010den \u017eivec<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n<p>V redkih primerih je fibrozna displazija lahko povezana z abnormalnostmi v \u017elezah, ki proizvajajo hormone endokrinega sistema. Abnormalnosti so lahko:<\/p>\n<ul>\n<li><\/li>\n<li>Zelo zgodnja puberteta<\/li>\n<li>Te\u017eave s \u0161\u010ditnico<\/li>\n<li>Svetlo rjave pege na ko\u017ei<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n<h2 id=\"vzroki\">Vzroki<\/h2>\n<p>Fibrozna displazija je genetska motnja, ki je povezana z mutacijo gene, ki proizvaja kosti. Mutacija nastane po spo\u010detju, v zgodnjih stopnjah razvoja zarodka. To pomeni, da mutacija ni podedovana s strani star\u0161ev, ter da se ne more prenesti na otroke.<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"zapleti\">Zapleti<\/h2>\n<p>Zaradi hude fibrozne displazije lahko nastanejo naslednji zapleti:<\/p>\n<p>&nbsp;<\/p>\n<ul>\n<li>Deformacija ali zlom kosti: oslabljeno obmo\u010dje prizadete kosti lahko povzro\u010di upogib kosti, kar pove\u010duje tveganje za nastanek zloma.<\/li>\n<li>Izguba vida in sluha: prizadeta kost je lahko zraven o\u010desnih ali slu\u0161nih \u017eivcev. V redkih primerih lahko huda deformacija obraznih kosti vodi do izgube vida in sluha.<\/li>\n<li>Artritis: deformacije v nogah in medeni\u010dnih kosteh lahko vodijo do razvoja artritisa sklepov teh kosti.<\/li>\n<li>Rak: v redkih primerih lahko prizadeto obmo\u010dje postane rakavo. Ta zaplet ponavadi prizadane ljudi, ki so imeli predhodno terapijo z obsevanjem.<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n<h2 id=\"zdravljenje\">Zdravljenje<\/h2>\n<p>Blaga fibrozna displazija, ki ne povzro\u010da nobenih znakov ali simptomov, ima nizko tveganje za nastanek deformacij ali zloma kosti. Vendar se stanje mora nadzorovati s periodi\u010dnimi rentgenskimi pregledi.<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"zdravila\">Zdravila<\/h2>\n<p>&nbsp;<\/p>\n<p>Zdravila za osteoporozo lahko pomagajo pri oja\u010danju prizadetih kosti, ki jih je prizadela fibrozna displazija. To lahko pomaga pri laj\u0161anju bole\u010dine in zmanj\u0161a tveganje za nastanek zloma.<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"operacija\">Operacija<\/h2>\n<p>&nbsp;<\/p>\n<p>Operacija je lahko ustrezno zdravljenje za:<\/p>\n<p>&nbsp;<\/p>\n<ul>\n<li>Popravilo deformacije<\/li>\n<li>Popravilo razlike v dol\u017eini udov<\/li>\n<li>Popravilo zloma<\/li>\n<li>Odstranitev prizadetega dela kosti (lezija), ki povzro\u010da te\u017eave<\/li>\n<li>Olaj\u0161anje pritiska na \u017eivec, \u0161e posebej \u010de se lezija nahaja v lobanji ali obrazu<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n<p>Operacija lahko vklju\u010duje odstranitev lezije na kosti, da se jo potem zamenja s kostjo, ki smo jo vzeli iz drugega dela telesa ali kostnega tkiva od darovalca. Kirurg lahko vstavi kovinske plo\u0161\u010de, palice ali vijake, da stabilizira kost. Tveganje povezano z operacije vklju\u010duje oku\u017ebo, krvni strdek in krvavitev.<\/p>\n","protected":false},"featured_media":0,"template":"","class_list":["post-72768","disease","type-disease","status-publish","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v24.3 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Fibrozna displazija - Humanitas.net<\/title>\n<meta name=\"robots\" content=\"noindex, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<meta property=\"og:locale\" content=\"sl_SI\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Fibrozna displazija - Humanitas.net\" \/>\n<meta property=\"og:description\" content=\"Fibrozna displazija je redka motnja kosti, pri kateri se namesto normalne kosti razvije brazgotinasto tkivo (fibrozno). To lahko oslabi kost in povzro\u010di, da se kost deformira ali po\u010di. 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