{"id":70393,"date":"2017-05-15T15:15:02","date_gmt":"2017-05-15T15:15:02","guid":{"rendered":"http:\/\/humanitasnet-new.local\/malattie\/imunodeficiente-comune-variabile\/"},"modified":"2025-01-13T02:43:16","modified_gmt":"2025-01-13T02:43:16","slug":"imunodeficiente-comune-variabile","status":"publish","type":"disease","link":"https:\/\/humanitas-net.humweb.webiz.team\/ro\/diseases\/imunodeficiente-comune-variabile\/","title":{"rendered":"Imunodeficien\u021be comune variabile"},"content":{"rendered":"<p>Imunodeficien\u021be comune variabile (CVID) este definit\u0103 ca o disfunc\u021bie a sistemului imunitar cauzat\u0103 de obicei de o muta\u0163ie &icirc;ntr-o gen\u0103 sau gene, &icirc;n care mai multe dintre proteine \u200b\u200b (anticorpi) care ajut\u0103 &icirc;n lupta &icirc;mpotriva infec\u021biilor sunt la un nivel sc\u0103zut. Persoanele cu CVID sunt foarte susceptibili la infec\u021bii, &icirc;n special &icirc;n c\u0103ile respiratorii, sinusuri \u0219i urechi.. CVID se caracterizeaz\u0103 printr-un nivel sc\u0103zut de proteine \u200b\u200bspecifice (anticorpi), de asemenea, numite imunoglobuline, care are ca rezultat un capacitate sc\u0103zut\u0103 pentru a combate microorganismele invadatoare, toxine sau alte substan\u021be str\u0103ine. Aceste imunoglobuline sunt produse de celule specializate albe (celule B), deoarece acestea ajung la maturitate.<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"simptome\">Simptome<\/h2>\n<p>Semnele \u0219i simptomele CVID pot ap\u0103rea &icirc;n timpul copil\u0103riei sau adolescen\u021bei. Semnele \u0219i simptomele CVID includ:<\/p>\n<ul>\n<li>Infec\u021bii ale urechii recursive<\/li>\n<li>Infec\u021bii ale sinusurilor recursive<\/li>\n<li>Recuren\u0163e infec\u021bii pulmonare<\/li>\n<li>Pneumonie<\/li>\n<li>Infec\u021bii bron\u0219ice recursive<\/li>\n<li>Infec\u021bii gastro-intestinale<\/li>\n<li>Articula\u021bii umflate dureroase<\/li>\n<li>Umflarea genunchi<\/li>\n<li>Glezn\u0103 umflat\u0103<\/li>\n<li>Umflarea cotului<\/li>\n<li>Umflarea &icirc;ncheietura m&acirc;inii<\/li>\n<li>Simptomele digestive<\/li>\n<li>Splin\u0103 m\u0103rit\u0103<\/li>\n<li>Glande umflate<\/li>\n<li>Noduli limfatici umfla\u021bi<\/li>\n<li>Boal\u0103 autoimun\u0103<\/li>\n<li>Infec\u0163ii ale sinusurilor<\/li>\n<li>Infec\u021bii ale urechii<\/li>\n<li>Conjunctivit\u0103<\/li>\n<li>Infec\u021bii respiratorii<\/li>\n<li>Diaree<\/li>\n<li>Meningit\u0103<\/li>\n<li>Limfadenopatie<\/li>\n<li>Num\u0103rul sc\u0103zut de celule plasmatice din m\u0103duva osoas\u0103<\/li>\n<li>Disfunc\u021bia celulelor T<\/li>\n<li>Bron\u015fit\u0103<\/li>\n<li>Diaree cronic\u0103<\/li>\n<li>Nivelele reduse IgA<\/li>\n<li>Nivelele reduse de IgG<\/li>\n<li>Nivelele reduse de IgM<\/li>\n<li>Lipsa nivelurilor normale de anticorpi<\/li>\n<li>Infec\u021bii recurente cronice&nbsp;<\/li>\n<li>Prezen\u021ba anticorpilor anti-IgA<\/li>\n<\/ul>\n<p>Semnele \u0219i simptomele CVID pot varia pe o baz\u0103 individual\u0103.<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"cauze\">Cauze<\/h2>\n<p>&nbsp;Cauza principal\u0103 a CVID este necunoscut\u0103, din cauza eterogenitatea bolii. Imunodeficien\u021be comune variabile se crede c\u0103 au rezultat dintr-o combina\u0163ie de factori genetici \u0219i de mediu. Condi\u021bia poate fi mo\u0219tenit\u0103 sau poate fi cauzat\u0103 de utilizarea anumitor medicamente antireumatice sau antiepileptice.<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"factori-de-risc\">Factori de risc<\/h2>\n<p>Cei mai mul\u021bi pacien\u021bi cu imunodeficien\u021b\u0103 variabil\u0103 comun\u0103 dezvolt\u0103 infec\u021bii bacteriene frecvente ale urechilor, sinusurilor, bronhiilor \u0219i a pl\u0103m&acirc;nilor. De asemenea, ei au de obicei o splin\u0103 m\u0103rit\u0103 \u015fi umflarea glandelor sau ganglionilor limfatici. Pacien\u021bii pot dezvolta articula\u021bii dureroase umflate &icirc;n genunchi, glezn\u0103, cot, sau &icirc;ncheieturii m&acirc;inii \u0219i, de asemenea, pot dezvolta tulbur\u0103ri digestive. &Icirc;mpreun\u0103 cu alte probleme autoimune, unii pacien\u0163i dezvolt\u0103 autoanticorpi care atac\u0103 propriile lor celule sanguine. Pacien\u021bii CVID au un risc crescut de a dezvolta anumite tipuri de cancer.<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"complicatii\">Complica\u0163ii<\/h2>\n<p>Pacien\u021bii CVID pot dezvolta complica\u021bii de diferite tipuri, cum ar fi:<\/p>\n<p>Manifest\u0103rile autoimunitare<\/p>\n<p>Autoimunitatea este principalul tip de complica\u021bie la pacien\u021bii CVID: anemie, anemie hemolitic\u0103 autoimun\u0103, purpur\u0103 trombocitopenic\u0103 idiopatic\u0103, psoriazis, vitiligo, artrit\u0103 reumatoid\u0103, hipotiroidism primar, gastrit\u0103 atrofic\u0103, maligne, &icirc;n special non-Hodgkin \u0219i carcinomul gastric;<\/p>\n<p>Enteropatia<\/p>\n<p>Simptomele CVID enteropatiei sunt similare cu cele ale boala celiac\u0103, de obicei &icirc;nso\u021bit\u0103 de simptome, cum ar fi crampe abdominale, diaree, constipa\u021bie \u0219i, &icirc;n unele cazuri, malabsorb\u0163ia \u015fi pierderea &icirc;n greutate.<\/p>\n<p>Infiltrare limfocitar\u0103 a \u021besuturilor<\/p>\n<p>Aceast\u0103 condi\u021bie provoac\u0103 umflarea ganglionilor limfatici, m\u0103rirea splinei \u0219i a ficatului, precum \u0219i formarea de granuloame.<\/p>\n<p>Anxietatea \u015fi depresia pot dezvolta, de asemenea, aceste simptome.<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"preventie\">Preven\u021bie<\/h2>\n<p>Nu exist\u0103 nici o cale de a preveni tulbur\u0103rile imunodeficien\u021bei congenitale. Dar nu toate persoanele care mo\u015ftenesc o muta\u0163ie a genei asociate cu CVID va dezvolta boala. Factorii genetici sau de mediu suplimentari sunt necesari, probabil pentru ca tulburare s\u0103 aib\u0103 loc, pentru c\u0103 &icirc;n multe cazuri, copiii afecta\u0163i au un p\u0103rinte neafectat, care &icirc;mp\u0103rt\u0103\u0219e\u0219te aceea\u0219i muta\u021bie. O nutri\u021bie bun\u0103 poate preveni imunodeficien\u0163a cauzat\u0103 de malnutri\u021bie.<\/p>\n","protected":false},"featured_media":0,"template":"","class_list":["post-70393","disease","type-disease","status-publish","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v24.3 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Imunodeficien\u021be comune variabile - Humanitas.net<\/title>\n<meta name=\"robots\" content=\"noindex, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<meta property=\"og:locale\" content=\"ro_RO\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Imunodeficien\u021be comune variabile - Humanitas.net\" \/>\n<meta property=\"og:description\" content=\"Imunodeficien\u021be comune variabile (CVID) este definit\u0103 ca o disfunc\u021bie a sistemului imunitar cauzat\u0103 de obicei de o muta\u0163ie &icirc;ntr-o gen\u0103 sau gene, &icirc;n care mai multe dintre proteine \u200b\u200b (anticorpi) care ajut\u0103 &icirc;n lupta &icirc;mpotriva infec\u021biilor sunt la un nivel sc\u0103zut. 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