{"id":72521,"date":"2019-01-31T13:56:36","date_gmt":"2019-01-31T13:56:36","guid":{"rendered":"http:\/\/humanitasnet-new.local\/malattie\/aphasie-primaire-progressive\/"},"modified":"2025-01-13T03:13:41","modified_gmt":"2025-01-13T03:13:41","slug":"aphasie-primaire-progressive","status":"publish","type":"disease","link":"https:\/\/humanitas-net.humweb.webiz.team\/fr\/diseases\/aphasie-primaire-progressive\/","title":{"rendered":"Aphasie primaire progressive"},"content":{"rendered":"<p>L&#8217;aphasie primaire progressive (APP) est un syndrome rare du syst\u00e8me neurologique qui affecte les capacit\u00e9s langagi\u00e8res. Il s&#8217;agit d&#8217;un type de d\u00e9g\u00e9n\u00e9rescence frontotemporale, un ensemble de troubles connexes qui prennent naissance dans les lobes frontaux ou temporaux du cerveau. Les personnes qui souffrent de ce syndrome peuvent avoir de la difficult\u00e9 \u00e0 exprimer leurs pens\u00e9es et \u00e0 comprendre ou \u00e0 trouver des mots. Cependant, ils peuvent continuer \u00e0 prendre soin d&#8217;eux-m\u00eames et \u00e0 participer aux activit\u00e9s de la vie quotidienne pendant plusieurs ann\u00e9es apr\u00e8s l&#8217;apparition de la maladie, \u00e0 mesure que le trouble \u00e9volue lentement.<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"symptomes\">Sympt\u00f4mes<\/h2>\n<p>Les personnes atteintes d&#8217;APP peuvent \u00e9prouver diff\u00e9rents types de sympt\u00f4mes du langage qui commencent graduellement et qui ont tendance \u00e0 s&#8217;aggraver avec le temps.\u00a0 Dans de nombreux cas, la premi\u00e8re indication que quelque chose ne va pas peut d&#8217;abord \u00eatre attribu\u00e9e au stress ou \u00e0 l&#8217;anxi\u00e9t\u00e9. Les sympt\u00f4mes de l&#8217;APP peuvent varier d&#8217;une personne \u00e0 l&#8217;autre, selon la partie du centre du langage du cerveau qui est touch\u00e9e. Ils \u00e9prouvent d&#8217;abord un ou plusieurs des sympt\u00f4mes suivants :<\/p>\n<ul>\n<li>Parole lente ou haletante ;<\/li>\n<li>Diminution de l&#8217;utilisation de la langue ;<\/li>\n<li>Des h\u00e9sitations \u00e0 trouver des mots ;<\/li>\n<li>Phrases dont l&#8217;ordre des mots est anormal dans le discours ou les courriels ;<\/li>\n<li>Utiliser des mots mal prononc\u00e9s ou incompr\u00e9hensibles ;<\/li>\n<li>Difficult\u00e9 \u00e0 comprendre ou \u00e0 suivre la conversation malgr\u00e9 une audition normale ;<\/li>\n<li>Perte soudaine de compr\u00e9hension de mots simples ;<\/li>\n<li>Oublier les noms d&#8217;objets familiers ;<\/li>\n<li>Incapacit\u00e9 de penser aux noms des personnes, m\u00eame si la personne est reconnue ;<\/li>\n<li>Probl\u00e8mes d&#8217;\u00e9criture, d&#8217;orthographe et de lecture ;<\/li>\n<li>Probl\u00e8mes d&#8217;arithm\u00e9tique et de calcul.<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n<h2 id=\"causes\">Causes<\/h2>\n<p>L&#8217;aphasie primaire progressive est caus\u00e9e par une atrophie des lobes frontaux et temporaux du cerveau, principalement du c\u00f4t\u00e9 gauche du cerveau, c&#8217;est-\u00e0-dire les parties du cerveau qui contr\u00f4lent la parole et le langage. L&#8217;aphasie primaire progressive affecte le centre du langage dans le cerveau. Des tissus cicatriciels et des prot\u00e9ines anormales peuvent \u00e9galement \u00eatre pr\u00e9sents, et l&#8217;activit\u00e9 c\u00e9r\u00e9brale est souvent r\u00e9duite.<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"facteurs-de-risque\">Facteurs de risque<\/h2>\n<p>Il n&#8217;existe aucun facteur de risque environnemental connu pour les aphasies progressives. Toutefois, une \u00e9tude observationnelle r\u00e9trospective a sugg\u00e9r\u00e9 que la vasectomie pourrait \u00eatre un facteur de risque d&#8217;AAP chez les hommes. Ces r\u00e9sultats n&#8217;ont pas encore \u00e9t\u00e9 reproduits ou d\u00e9montr\u00e9s par des \u00e9tudes prospectives. L&#8217;APP n&#8217;est pas consid\u00e9r\u00e9e comme une maladie h\u00e9r\u00e9ditaire. Cependant, les parents d&#8217;une personne atteinte d&#8217;une forme quelconque de d\u00e9g\u00e9n\u00e9rescence lobaire frontotemporale sont l\u00e9g\u00e8rement plus \u00e0 risque de d\u00e9velopper une APP ou une autre forme de la maladie.<\/p>\n<p>Les facteurs de risque de l&#8217;aphasie primaire progressive comprennent les troubles d&#8217;apprentissage et certaines mutations g\u00e9n\u00e9tiques.<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"complications\">Complications<\/h2>\n<p>Au fur et \u00e0 mesure que la maladie progresse, d&#8217;autres habilet\u00e9s mentales, comme la m\u00e9moire, peuvent devenir alt\u00e9r\u00e9es. Certaines personnes peuvent d\u00e9velopper d&#8217;autres troubles neurologiques avec le temps. Si ces complications surviennent, la personne atteinte aura \u00e9ventuellement besoin d&#8217;aide pour les soins quotidiens. Certaines personnes atteintes d&#8217;une APP peuvent devenir muettes et finir par perdre la capacit\u00e9 de comprendre la langue \u00e9crite et parl\u00e9e.<\/p>\n<p>Les personnes atteintes d&#8217;aphasie progressive primaire peuvent \u00e9galement d\u00e9velopper des probl\u00e8mes comportementaux ou sociaux, comme l&#8217;anxi\u00e9t\u00e9 ou l&#8217;irritabilit\u00e9. D&#8217;autres probl\u00e8mes peuvent inclure des \u00e9motions \u00e9mouss\u00e9es, un mauvais jugement ou un comportement social inappropri\u00e9.<\/p>\n","protected":false},"featured_media":0,"template":"","class_list":["post-72521","disease","type-disease","status-publish","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v24.3 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Aphasie primaire progressive - Humanitas.net<\/title>\n<meta name=\"robots\" content=\"noindex, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<meta property=\"og:locale\" content=\"fr_FR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Aphasie primaire progressive - Humanitas.net\" \/>\n<meta property=\"og:description\" content=\"L&#8217;aphasie primaire progressive (APP) est un syndrome rare du syst\u00e8me neurologique qui affecte les capacit\u00e9s langagi\u00e8res. 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