{"id":72502,"date":"2019-01-31T13:34:21","date_gmt":"2019-01-31T13:34:21","guid":{"rendered":"http:\/\/humanitasnet-new.local\/malattie\/polycythemia-vera-2\/"},"modified":"2025-01-13T03:13:24","modified_gmt":"2025-01-13T03:13:24","slug":"polycythemia-vera","status":"publish","type":"disease","link":"https:\/\/humanitas-net.humweb.webiz.team\/fr\/diseases\/polycythemia-vera\/","title":{"rendered":"Polycyth\u00e9mia vera"},"content":{"rendered":"<p>La polycythemia vera (ou maladie de Vaquez) est un type rare de cancer du sang \u00e0 croissance lente dans lequel la moelle osseuse fabrique trop de globules rouges. La polycyth\u00e9mia vera peut \u00e9galement entra\u00eener la production d&#8217;un trop grand nombre d&#8217;autres types de cellules sanguines \u2014 globules blancs et plaquettes. Ces cellules en exc\u00e8s \u00e9paississent le sang et provoquent des complications, telles qu&#8217;un risque de caillots sanguins ou de saignement.<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"symptomes\">Sympt\u00f4mes<\/h2>\n<p>Puisqu&#8217;elle se d\u00e9veloppe habituellement lentement, le patient peut l&#8217;avoir pendant des ann\u00e9es sans remarquer de signes ou de sympt\u00f4mes. Pour de nombreux patients, la polycyth\u00e9mia vera peut m\u00eame ne causer aucun signe ou sympt\u00f4me. Cependant, certaines personnes peuvent d\u00e9velopper les sympt\u00f4mes suivants :<\/p>\n<ul>\n<li>Hypertension art\u00e9rielle ;<\/li>\n<li>Maux de t\u00eate et vision floue ;<\/li>\n<li>\u00c9tourdissements ;<\/li>\n<li>Faiblesse ;<\/li>\n<li>Transpiration excessive ;<\/li>\n<li>Malaise dans l&#8217;abdomen ;<\/li>\n<li>Enflure douloureuse d&#8217;une articulation, souvent le gros orteil ;<\/li>\n<li>Difficult\u00e9 \u00e0 respirer lorsque les patients s&#8217;allongent ;<\/li>\n<li>Engourdissement, picotement, br\u00fblure ou faiblesse dans les mains, les pieds, les bras ou les jambes ;<\/li>\n<li>Une sensation de rondeur ou de ballonnement dans la partie sup\u00e9rieure gauche de l&#8217;abdomen en raison d&#8217;une hypertrophie de la rate ;<\/li>\n<li>Peau rouge, en particulier sur le visage, les mains et les pieds ;<\/li>\n<li>Probl\u00e8mes de saignement \u2013 tels que saignements de nez et ecchymoses ;<\/li>\n<li>La goutte, qui peut causer des douleurs articulaires, de la raideur et des gonflements.<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n<h2 id=\"causes\">Causes<\/h2>\n<p>Polycyth\u00e9mia vera survient lorsqu&#8217;une mutation dans une cellule de la moelle osseuse cause un probl\u00e8me au niveau de la production des cellules sanguines. Normalement, l&#8217;organisme r\u00e8gle avec soin le nombre de chacun des trois types de cellules sanguines. Cependant, dans les cas de polycythemia vera, ce m\u00e9canisme de r\u00e9gulation est endommag\u00e9 et la moelle osseuse fabrique trop de certaines cellules sanguines. On pense que la mutation qui cause la polycythemia vera affecte un commutateur prot\u00e9ique qui stimule la croissance des cellules. La plupart des personnes atteintes de polycythemia vera ont ce type de mutation. Les causes des mutations ne sont pas claires, mais les chercheurs croient qu&#8217;elles surviennent apr\u00e8s la conception, de sorte qu&#8217;elles sont acquises plut\u00f4t qu&#8217;h\u00e9rit\u00e9es d&#8217;un parent.<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"facteurs-de-risque\">Facteurs de risque<\/h2>\n<p>Le risque de polycythemia vera augmente avec l&#8217;\u00e2ge. Elle est plus fr\u00e9quente chez les adultes de plus de 60 ans, bien que la maladie puisse survenir \u00e0 tout \u00e2ge.<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"complications\">Complications<\/h2>\n<p>En l&#8217;absence d&#8217;un traitement appropri\u00e9, la polycythemia vera peut mettre la vie en danger. Cependant, avec des soins m\u00e9dicaux appropri\u00e9s, de nombreuses personnes \u00e9prouvent peu de probl\u00e8mes li\u00e9s \u00e0 cette maladie. Avec le temps, il y a un risque d&#8217;\u00e9volution vers des cancers du sang plus graves, comme la my\u00e9lofibrose ou la leuc\u00e9mie aigu\u00eb.<\/p>\n<p>Les complications possibles de polycythemia vera incluent :<\/p>\n<ul>\n<li>Caillots de sang<\/li>\n<li>Agrandissement de la rate<\/li>\n<li>Probl\u00e8mes de peau<\/li>\n<li>Probl\u00e8mes dus \u00e0 des taux \u00e9lev\u00e9s de globules rouges<\/li>\n<li>Autres troubles sanguins<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n<h2 id=\"prevention\">Pr\u00e9vention<\/h2>\n<p>Malheureusement, il n&#8217;y a aucun moyen de pr\u00e9venir la polycythemia vera. Cependant, le risque de polycyth\u00e9mie secondaire peut \u00eatre r\u00e9duit par un mode de vie sain et en ne passant pas de longues p\u00e9riodes \u00e0 haute altitude. De plus, les sympt\u00f4mes et les complications peuvent \u00eatre pr\u00e9venus ou retard\u00e9s par un traitement appropri\u00e9.<\/p>\n","protected":false},"featured_media":0,"template":"","class_list":["post-72502","disease","type-disease","status-publish","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v24.3 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Polycyth\u00e9mia vera - Humanitas.net<\/title>\n<meta name=\"robots\" content=\"noindex, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<meta property=\"og:locale\" content=\"fr_FR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Polycyth\u00e9mia vera - Humanitas.net\" \/>\n<meta property=\"og:description\" content=\"La polycythemia vera (ou maladie de Vaquez) est un type rare de cancer du sang \u00e0 croissance lente dans lequel la moelle osseuse fabrique trop de globules rouges. 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