{"id":72427,"date":"2019-01-30T14:22:04","date_gmt":"2019-01-30T14:22:04","guid":{"rendered":"http:\/\/humanitasnet-new.local\/malattie\/maladie-surrenalienne-nodulaire\/"},"modified":"2025-01-13T03:12:16","modified_gmt":"2025-01-13T03:12:16","slug":"maladie-surrenalienne-nodulaire","status":"publish","type":"disease","link":"https:\/\/humanitas-net.humweb.webiz.team\/fr\/diseases\/maladie-surrenalienne-nodulaire\/","title":{"rendered":"Maladie surr\u00e9nalienne nodulaire"},"content":{"rendered":"<h2 id=\"introduction-quest-ce-quune-maladie-nodulaire-de-la-glande-surrenale\">Introduction : Qu&#8217;est-ce qu&#8217;une maladie nodulaire de la glande surr\u00e9nale ?<\/h2>\n<p>Les l\u00e9sions surr\u00e9naliennes nodulaires d&#8217;int\u00e9r\u00eat chirurgical sont nombreuses. Certaines d&#8217;entre elles, appel\u00e9es &#8220;l\u00e9sions surr\u00e9nales fonctionnelles&#8221; (ad\u00e9nomes, carcinomes, ph\u00e9ochromocytomes, etc.) peuvent se manifester avec certains syndromes hormonaux (syndrome de Cushing, syndrome de Conn, syndrome du ph\u00e9ochromocytome). D&#8217;autres ne s\u00e9cr\u00e8tent aucune hormone et sont donc appel\u00e9es &#8220;l\u00e9sions surr\u00e9naliennes non fonctionnelles&#8221; (par ex. ad\u00e9nomes et carcinomes non fonctionnels, my\u00e9lolipomes, kystes, etc.).<\/p>\n<p>&nbsp;<\/p>\n<h2 id=\"symptomes-comment-puis-je-savoir-si-je-souffre-dune-maladie-nodulaire-de-la-glande-surrenale\">Sympt\u00f4mes : comment puis-je savoir si je souffre d&#8217;une maladie nodulaire de la glande surr\u00e9nale ?<\/h2>\n<p>Les signes et sympt\u00f4mes des l\u00e9sions nodulaires de la glande surr\u00e9nale sont multiples et d\u00e9pendent 1) de l&#8217;hypers\u00e9cr\u00e9tion possible d&#8217;hormones et 2) de la taille de la masse. Dans de nombreux cas, cependant, cette maladie est diagnostiqu\u00e9e accidentellement au cours d&#8217;examens radiologiques au-del\u00e0 de la suspicion d&#8217;une maladie surr\u00e9nalienne (surr\u00e9nalome fortuit). Parmi les syndromes cliniques associ\u00e9s \u00e0 l&#8217;hypers\u00e9cr\u00e9tion hormonale, on trouve notamment :<\/p>\n<ul>\n<li>Le syndrome de Cushing : provoquant une hypers\u00e9cr\u00e9tion de cortisol par ad\u00e9nome, cancer ou hyperplasie micro\/macro nodulaire d&#8217;un ou des deux c\u00f4t\u00e9s, caract\u00e9ris\u00e9e par une ob\u00e9sit\u00e9 centrale, une bosse dorsale, une face pleine lune (arrondie), une pression art\u00e9rielle \u00e9lev\u00e9e, une faiblesse musculaire, une ost\u00e9op\u00e9nie\/porosit\u00e9, des \u00e9v\u00e9nements psychiatriques, hirsutisme, acn\u00e9, stries rubrae, peau fragile avec des ecchymoses faciles, troubles menstruels, baisse de la libido, impuissance, intol\u00e9rance au glucose ou diab\u00e8te sucr\u00e9, immunosuppression et pr\u00e9disposition aux infections, le risque de thrombose ;<\/li>\n<li>Hyperaldost\u00e9ronisme primaire : hypers\u00e9cr\u00e9tion d&#8217;aldost\u00e9rone soutenue par un ad\u00e9nome surr\u00e9nalien unilat\u00e9ral (syndrome de Conn) ou une hyperplasie nodulaire, mono ou bilat\u00e9rale, qui se manifeste g\u00e9n\u00e9ralement par une hypertension art\u00e9rielle, souvent r\u00e9sistante aux traitements pharmacologiques, et une hypokali\u00e9mie (qui n&#8217;est pas une condition pr\u00e9alable au diagnostic), entra\u00eenant crampes, paresth\u00e9sie, fatigue des muscles ;<\/li>\n<li>Syndrome du ph\u00e9ochromocytome : provoquant l&#8217;hypers\u00e9cr\u00e9tion des cat\u00e9cholamines, caract\u00e9ris\u00e9e par l&#8217;hypertension art\u00e9rielle associ\u00e9e \u00e0 une crise de palpitations, maux de t\u00eate, transpiration, p\u00e2leur, naus\u00e9es, anxi\u00e9t\u00e9, tremblements et hyperglyc\u00e9mie ;<\/li>\n<li>Syndrome de virilisation (acquisition de caract\u00e9ristiques masculines par les femmes, y compris hirsutisme, acn\u00e9, hypertrophie des muscles, perte de cheveux, hypertrophie du clitoris) ou f\u00e9minisation (augmentation du volume des seins, ou gyn\u00e9comastie, r\u00e9duction de la barbe et poils du corps chez les hommes) due \u00e0 la pr\u00e9sence de l\u00e9sions qui s\u00e9cr\u00e8tent des hormones m\u00e2les (androg\u00e8nes) ou femelles (\u0153strog\u00e8ne).<\/li>\n<\/ul>\n<p>&nbsp;<\/p>\n<h2 id=\"epidemiologie-quelle-est-la-frequence-des-maladies-nodulaires-de-la-glande-surrenale\">\u00c9pid\u00e9miologie : Quelle est la fr\u00e9quence des maladies nodulaires de la glande surr\u00e9nale ?<\/h2>\n<p>Les nodules surr\u00e9naliens sont une d\u00e9couverte fortuite tr\u00e8s fr\u00e9quente. On estime que 3 \u00e0 5 % de la population &#8220;en bonne sant\u00e9&#8221; est involontairement porteuse d&#8217;un ou plusieurs nodules surr\u00e9naliens. Dans la grande majorit\u00e9 des cas, ces nodules sont de petite taille et n&#8217;ont pas d&#8217;importance clinique et ne n\u00e9cessitent pas d&#8217;ablation. Les hormones s\u00e9cr\u00e9tantes ou les l\u00e9sions surr\u00e9nales malignes sont rares. Par exemple, le syndrome de Cushing a une incidence annuelle de 4 \u00e0 5 nouveaux cas par million d&#8217;habitants par an.<\/p>\n","protected":false},"featured_media":0,"template":"","class_list":["post-72427","disease","type-disease","status-publish","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v24.3 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Maladie surr\u00e9nalienne nodulaire - Humanitas.net<\/title>\n<meta name=\"robots\" content=\"noindex, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<meta property=\"og:locale\" content=\"fr_FR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Maladie surr\u00e9nalienne nodulaire - Humanitas.net\" \/>\n<meta property=\"og:description\" content=\"Introduction : Qu&#8217;est-ce qu&#8217;une maladie nodulaire de la glande surr\u00e9nale ? 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